What is pulmonary renal syndrome?

What is pulmonary renal syndrome?

Abstract. Pulmonary renal syndrome (PRS) describes the occurrence of renal failure in association with respiratory failure, characterised by autoimmune-mediated rapidly progressive glomerulonephritis (RPGN) and diffuse alveolar haemorrhage (DAH), respectively.

How does kidney disease cause pulmonary hypertension?

The increased pulse pressure resulting from decreased vascular compliance exacerbates the renal disease progression. Decreased pulmonary vascular compliance is a very early change in pulmonary hypertension. Perhaps, decreased vascular compliance is a common pathophysiological change in both circulations in CKD.

What is the life expectancy of Wegener’s disease?

The prognosis of wegener’s disease is not good. According to some studies, the life expectancy for it is 67.1+/- 4.4 months. Wegner’s granulomatosis is a kind of vasculitis that commonly involve the kidneys and lungs. The prognosis is dismal when both are involved.

What causes Wegener’s disease?

The exact cause of Wegener’s Disease (GPA) is currently unknown. It is believed to be an auto-immune disease, where the body mistakenly attacks it’s own tissues. In a similar way to other auto-immune diseases it is thought that there is a genetic component to Wegener’s.

What is Wagner’s disease?

Wegener’s granulomatosis is a very rare disease that affects many different organs and systems of the body. It mainly attacks the respiratory system (sinuses, nose, windpipe, and the lungs) and the kidneys. One of the main features of the disease is an inflammation of the blood vessels ( vasculitis ).

What is Wegener syndrome?

Overview. Formerly called Wegener’s granulomatosis, this condition is one of a group of blood vessel disorders called vasculitis. It slows blood flow to some of your organs. The affected tissues can develop areas of inflammation called granulomas, which can affect how these organs work.